Yilmaz Ovali G.Tarhan S.Bayindir P.Polat M.Akil I.2024-07-222024-07-22200913000144http://akademikarsiv.cbu.edu.tr:4000/handle/123456789/18670Congenital absence of Internal Carotid Artery (ICA) is a rare disorder. This anomaly may be an isolated entity or may be associated with other organ, or system anomalies (1). Multicystic Dysplastic Kidney (MCDK) is a congenital mal-development in which the renal cortex is replaced by numerous cysts of multiple sizes. Urologic and non-urologic anomalies may accompany MCDK (2). In this paper, we detail a case of congenital agenesis of ICA and the existence of MCDK. To our knowledge, this is the first of such a case to be reported regarding the co-occurrence of ICA agenesis and MCDK. © TÜBİTAK.EnglishAll Open Access; Bronze Open AccessHydraulic structuresIndependent component analysisAgenesisCarotid canalCo-occurrenceInternal carotid arteryRenal cortexarticlecarotid artery anomalycase reportclinical featurehumaninfantinternal carotid artery agenesislaboratory testmagnetic resonance angiographymalemulticystic dysplastic kidneynuclear magnetic resonance imagingphysical examinationHemodynamicsCo-occurrence of internal carotid artery agenesis with multicystic dysplastic kidneyArticle10.3906/sag-0706-11