Ovali, GYTarhan, SBayindir, PPolat, MAkil, I2024-07-182024-07-181300-01441303-6165http://akademikarsiv.cbu.edu.tr:4000/handle/123456789/4260Congenital absence of Internal Carotid Artery (ICA) is a rare disorder. This anomaly may be an isolated entity or may be associated with other organ, or system anomalies (1). Multicystic Dysplastic Kidney (MCDK) is a congenital mal-development in which the renal cortex is replaced by numerous cysts of multiple sizes. Urologic and non-urologic anomalies may accompany MCDK (2). In this paper, we detail a case of congenital agenesis of ICA and the existence of MCDK. To our knowledge, this is the first of such a case to be reported regarding the co-occurrence of ICA agenesis and MCDK.EnglishCONGENITAL HORNERS-SYNDROMEHYPOPLASIAArticle