Taneli C.Genc K.Erikci V.Balik E.Erhan Y.Ozdemir N.Veral A.2024-07-222024-07-22199610165142http://akademikarsiv.cbu.edu.tr:4000/handle/123456789/20674A 15-year-old girl was admitted to the pediatric surgery department with primary amenorrhea and right inguinal swelling of one year duration. On physical examination, the patient presented with a female phenotype, but no breast development; somewhat hirsute with hypertrophic clitoris. Ultrasound examination disclosed a palpable mass originating from the right ovary. At operation, a right salpingo-ooferectomy was performed, and a biopsy specimen was obtained from the left ovary which did not appear normal. Histopathologic examination revealed a right ovarian disgerminoma and a left gonadoblastoma. One month after the first operation, a left gonadectomy was performed with accompanying cliteroplasty. An original case of Swyer syndrome is reported in a patient with female phenotype, dysgerminoma of the right and gonadoblastoma of the the left ovaries.Englishadolescentarticlecase reportdysgerminomafemalegonadal dysgenesisgonadectomygonadoblastomahistopathologyhumanArticle