Incontinentia pigmenti Stage 1 is not simply vesiculo-bullous but vesiculo-pustular

dc.contributor.authorÇetinarslan T.
dc.contributor.authorFölster-Holst R.
dc.contributor.authorVan Gysel D.
dc.contributor.authorBuchner M.
dc.contributor.authorHapple R.
dc.date.accessioned2024-07-22T08:01:49Z
dc.date.available2024-07-22T08:01:49Z
dc.date.issued2024
dc.description.abstractIncontinentia pigmenti (IP) is a rare X-linked dominant, male-lethal disorder characterized by pathognomic skin lesions. As described in the literature the typical cutaneous changes follow the pattern of Blaschko's lines and develop in four stages that usually start at birth. Stage 1 is called vesicular, bullous or inflammatory. The vesicles are rapidly filled with eosinophils and thus turn into pustules. Thus, the term “pustular” is relevant to the first phase of IP, and the stage can be considered as “vesiculopustular/inflammatory” to be more precise than “vesicular” or “bullous.”. © 2023 Wiley Periodicals LLC.
dc.identifier.DOI-ID10.1111/pde.15465
dc.identifier.issn07368046
dc.identifier.urihttp://akademikarsiv.cbu.edu.tr:4000/handle/123456789/11576
dc.language.isoEnglish
dc.publisherJohn Wiley and Sons Inc
dc.subjectBlister
dc.subjectEosinophils
dc.subjectHumans
dc.subjectIncontinentia Pigmenti
dc.subjectInfant, Newborn
dc.subjectMale
dc.subjectRare Diseases
dc.subjectSkin
dc.subjectacne
dc.subjectacrodermatitis continua
dc.subjectArticle
dc.subjectbullous skin disease
dc.subjectcandidiasis
dc.subjectcentral nervous system
dc.subjectcongenital syphilis
dc.subjectdisease exacerbation
dc.subjecteosinophil
dc.subjectepidermolysis bullosa
dc.subjecteye
dc.subjectgene
dc.subjectgene mutation
dc.subjectgenodermatosis
dc.subjectherpes simplex
dc.subjecthistopathology
dc.subjecthuman
dc.subjectIKBKG gene
dc.subjectimpetigo
dc.subjectincontinentia pigmenti
dc.subjectinflammation
dc.subjectLangerhans cell histiocytosis
dc.subjectnail
dc.subjectnewborn
dc.subjectpustule
dc.subjectscabies
dc.subjectskin
dc.subjectskin defect
dc.subjectstaging
dc.subjectStaphylococcus infection
dc.subjecttooth
dc.subjectvesiculopustule
dc.subjectX chromosome linked disorder
dc.subjectblister
dc.subjectincontinentia pigmenti
dc.subjectmale
dc.subjectpathology
dc.subjectrare disease
dc.titleIncontinentia pigmenti Stage 1 is not simply vesiculo-bullous but vesiculo-pustular
dc.typeArticle

Files