Percutaneous embolization of congenital portosystemic venous shunt in an infant with respiratory distress
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Date
2018
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Abstract
A 5-month-old boy with progressive respiratory distress was admitted to our hospital. Physical examination revealed mild tachypnea and retraction. The left main bronchus was found as severely collapsed between the right pulmonary artery and the descending aorta, on the bronchoscopic evaluation. Further evaluation revealed persistent ductus venosus (PDV). As in the fetal period the ductus venosus arises from the posterior aspect of the left portal vein, a PDV is considered another type of intrahepatic portosystemic shunt. Therefore, he was diagnosed with congenital portosystemic venous shunt, leading to persistent respiratory distress. The PDV was closed with Amplatzer vascular plug II, and then he had immediate clinical improvement. Congenital portosystemic venous shunts (CPSS) are rare vascular malformations associated with severe complications. Here we presented a case with progressive respiratory distress as a result of CPSS and rapid improvement after embolization. © 2018, Turkish Journal of Pediatrics. All rights reserved.
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Bronchoscopy , Embolization, Therapeutic , Humans , Infant , Male , Portal Vein , Respiratory Distress Syndrome, Adult , Tomography, X-Ray Computed , Ultrasonography, Doppler , Vascular Malformations , acetylsalicylic acid , angiography , Article , artificial embolization , balloon occlusion , bronchoscopy , case report , clinical article , computed tomographic angiography , congenital portosystemic shunt , coronary vein , coughing , device embolization , Doppler ultrasonography , echocardiography , heart catheterization , heart ventricle size , hepatomegaly , human , infant , inferior cava vein , lung circulation , main bronchus , male , oxygen saturation , percutaneous embolization , persistent ductus venosus , pulse rate , respiratory distress , tachypnea , thorax radiography , vein aneurysm , abnormalities , adult respiratory distress syndrome , artificial embolization , complication , congenital blood vessel malformation , hepatic portal vein , procedures , x-ray computed tomography